Male adrenoleukodystrophy phenotypes[1]
Phenotype Description Onset Approximate Relative Frequency
Childhood cerebral Progressive neurodegenerative decline, leading to a vegetative state without treatment 3–10 years 31–35%
Adolescent Similar to childhood cerebral, with a slower progression 11–21 years 4–7%
Adrenomyeloneuropathy (AMN) Progressive neuropathy, paraparesis; approximately 40% progress to cerebral involvement 21–37 years 40–46%
Adult cerebral Dementia, behavioral disturbances, similar progression to childhood cerebral form, but without preceding AMN phenotype Adulthood 2–5%
Olivo-ponto-cerebellar Cerebral and brain stem involvement Adolescence to adulthood 1–2%
"Addison disease only" Adrenal insufficiency Before 7.5 years Up to 50% in childhood, varies with age
Asymptomatic No clinical presentation, further studies can reveal subclinical adrenal insufficiency or mild AMN phenotype Most common phenotype in boys under four years of age Proportion of asymptomatic patients decreases with age
   
advanced
Trip   Boat used on second leg
Overall Length 2300km/1241 naut. miles   Yole Class, by Virus -Fiberglass
1. leg 2003 400km/ 220 naut. miles   Length: 4.80meter / 15'9"
2. leg 2005 1900km/1025 naut. miles   Width: 83cm / 33"
Days on the water: 109   Weight: 60kg / 125lbs
Hours rowed: 550   Rigger Span: 158cm/ 62"
Longest leg 29 hours /140km/76 n.miles   Cockpit open, 100% self bailing
Total burn of energy (body) Kcal 500.000 = 70 kg/150lbs Butter   Manufacturer Yole: Virus, France
Average Air temp: 10 degrees celcius   Oars Carbon/ Hatchet Blades
Water temp: 2 -10 degrees celcius   Spare Oars Aluminum, Macon Blades
Average daylight: June=24h > Sept=17h    
     
Money raised for Iceland Handicaped Association = 8.5 M Iceland Kroner = USD 135,000.00 (Pop. of Iceland 300,000)

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Male adrenoleukodystrophy phenotypes[1]
Phenotype Description Onset Approximate Relative Frequency
Childhood cerebral Progressive neurodegenerative decline, leading to a vegetative state without treatment 3–10 years 31–35%
Adolescent Similar to childhood cerebral, with a slower progression 11–21 years 4–7%
Adrenomyeloneuropathy (AMN) Progressive neuropathy, paraparesis; approximately 40% progress to cerebral involvement 21–37 years 40–46%
Adult cerebral Dementia, behavioral disturbances, similar progression to childhood cerebral form, but without preceding AMN phenotype Adulthood 2–5%
Olivo-ponto-cerebellar Cerebral and brain stem involvement Adolescence to adulthood 1–2%
"Addison disease only" Adrenal insufficiency Before 7.5 years Up to 50% in childhood, varies with age
Asymptomatic No clinical presentation, further studies can reveal subclinical adrenal insufficiency or mild AMN phenotype Most common phenotype in boys under four years of age Proportion of asymptomatic patients decreases with age
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